Isikhumba se-pemphigoid noma Isifo se-Lever yisimo esingapheli sezilonda zesikhumba nokubunjwa kwe-blisters. Ngokuvamile, lesi sifo senzeke kubantu asebekhulile, abaneminyaka engama-60 nangaphezulu, okungajwayelekile kakhulu ekufeni kwesifo seLevera esibhekene nezingane. Kulesi simo, i-pemphigoid iyingozi, futhi isithombe somtholampilo sifana kakhulu ne-pemphigus engcolile, okuyizinga elithile eliyinkimbinkimbi yokuxilongwa nokukwelashwa.
Izimpawu ze-pemphigoid enezinkunzi
Ngokuvame ukuthi lesi sifo sithinta isikhumba se-trunk kanye neziphetho, okungajwayelekile kakhulu ukuthi i-pemphigoid ihlanganisa izicubu zekhanda, ubuso nezinqwaba zemvelo. Isici sesifo sikaLerara yizimphambaniso ezilinganiselwe, okungukuthi:
- amabhulogi ;
- vesicles.
Iqukethe uketshezi olucacile, oluvinjelwe ngamathayi ahlukumezekile. Kuyinto engavamile esikhumbeni lapho amabhuleki abonakala enemibala enempilo, kodwa kaningi ephuza ukubomvu okuhambisanayo, okubuye kube uphawu lwesifo. Isithombe sesitholampilo sisekelwa yi-blisters yobukhulu obuhlukahlukene, okungabonakalisa ngephutha i-sarcoidosis.
Izimpawu ezibhalwe phansi ziyinhloko futhi zizibonakalisa ezinsukwini ezimbalwa zokuqala, ngemva kwalokho ukuvuvukala nezibhansela zivulwa futhi izifo ezinamaqabunga ezilonda-mganga zenziwa endaweni yazo. Endabeni ye-pemphigod enezinyosi, izilonda azihlanganiswa nama-crusts, kodwa zi-epithelialized.
Kubuye kubalulekile ukuthi kulesi siguli esisodwa kwezingu-5 ukuhlaselwa kuhlasela ngokuyinhloko i-mucosa yomlomo futhi kuvela kuphela esikhumbeni.
Ukwelashwa kwe-pemphigoid enezinkunzi
Ukungafani kokwelashwa kwesifo se-pemphigoid noma isifo seLever kuwukuthi kufanele kube yinkimbinkimbi futhi umuntu ngamunye. Odokotela bakhethe umuthi wokwelashwa ngokusekelwe kumaqiniso alandelayo:
- ukuqina kwesigaba sesifo;
- ukusakazeka kwenqubo;
- ukutholakala kwezifo ezithintekayo;
- isimo jikelele sesiguli.
Kodwa kunoma yikuphi, izindlela eziyinhloko zokwelapha isifo sikaLever ziyimithi equkethe i-glucocorticosteroids. Ekuqaleni kokwelashwa, iziguli zinikeze u-60-80 mg wezidakamizwa emahoreni angu-24. Emva kwalokhu, udokotela, ngokucabangela idatha engenhla, ushintshe umthamo.
Okunye okusetshenziselwa ukwelashwa kwe-pemphigoid, i- immunosuppressants kanye ne-cytostatics. Lezi zidakamizwa zivimbela ukuzivikela, futhi zisuse isisu. Ngokuya ngobukhulu bezimpawu kanye nesigaba sokuthuthukiswa kwazo, ama-enzyme ahleliwe anqunywe, amalungiselelo akhiwe ngokuhlanganiswa kwezitshalo ezinamapulazi nezitshalo ezithinta izinqubo zokuvuvukala, izinqubo zokubuyisela kanye nezimpendulo zomzimba. Ngakho, isimo sesiguli sithuthukiswa kakhulu.