Ngokuvamile, isifo sikaTayasuasu sithinta abesifazane abaneminyaka engama-15 no-30 abanamakhosikazi aseMongooloid. Isilinganiso salesi sigaba sesiguli kuya kwabanye cishe ngo-8: 1. Isifo esivame kakhulu sibonakala kwabesifazane abahlala eJapane, kodwa lokhu akusho ukuthi siphephile ngokuphelele. I-aortoarteritis engavamile, njengoba le nsizwa ibizwa futhi, isanda kubhalwa eYurophu.
Izimpawu zesifo sikaTakayasu
I-Arteritis Takayasu yisifo esiqala ngenqubo yokuvuvukala ezindongeni ze-aorta, futhi umsuka wale syndrome awusungulwa kuze kube manje. Kwakukhona iziphakamiso ukuthi lesi sifo sinesimo semvelo, kodwa asizange sithole isiqinisekiso. Cishe, i-aortoarteritis engavamile, noma isifo se-Takayasu, isuke isuka ku-genetic.
Inqubo yokuvuvukala ithinta izindonga ze-aorta kanye nemithambo emikhulu, amangqamuzana amakhulu aqala ukubuthelela kuwo, ngenxa yalokho isibani esinciphisa futhi ukujikeleza okuvamile kuphazamiseka. Esigabeni sokuqala sesi sifo, kunezibonakaliso ezivamile ze-somatic:
- umkhuhlane;
- isiyezi nosizi;
- ubuthakathaka jikelele;
- izinkinga ezahlukene zokulala;
- ukunganakwa;
- ukulahlekelwa kwesisindo ngokushesha;
- ukuphulukisa ubuhlungu obuhlanganyelwe kanye nokwehliswa kwamalungu .
Izimpawu ezengeziwe ze-arteritis Takayasu zibonakaliswa kuye ngokuthi yiziphi izinzwa ezithintekayo kakhulu:
- Lapho i-brachiocephalic trunk ilimele, imishanguzo ye-carotid ne-subclavia ilahlekelwa yi-pulse ezandleni zabo.
- Uma i-aorta yesisu nesisu isithinteka, i-stenosis ye-atypical iyabonakala.
- Ukuhlanganiswa kwezimpawu zohlobo lokuqala nolwesibili.
- Ukwandiswa kwemikhumbi, okuholela ekwandiseni i-aorta namagatsha ayo amakhulu.
Ngenxa yalokho, isifo senhliziyo siqala ukuthuthukisa, ikakhulukazi i-angina ne-sciatica. Ngaphandle kokwelashwa okufanele, ukufa kubangelwa ukuhluleka kwe-valve senhliziyo, noma ingozi ye-cerebrovascular.
Ukwelashwa kwesifo se-Takayasu
Ukuthola isifo se-Takayasu kuhlanganisa ukuhlolwa kwe-ultrasound nokuhlolwa kwegazi. Uma lesi sifo sitholakale ngesikhathi futhi kufanele siphathwe ngendlela efanele, singena kwifomu elingapheli futhi asiqhubeki. Lokhu kunikeza isiguli iminyaka eminingi yokuphila okuvamile.
Ukwelapha i-arteritis ka-Takayasu kuhlanganisa nokusetshenziswa ngendlela ehlelekile kwe- corticosteroids , ngokuvamile i-Prednisolone. Ezinyangeni ezimbalwa zokuqala, isiguli sinikezwa isilinganiso esiphezulu, bese sinciphisa inani eliphansi elanele ukukhulula ukuvuvukala. Ngemuva konyaka, ungayeka ukuthatha izidakamizwa eziphikisayo.