Kunezinhlobo eziningana ze-vasculitis yesistimu, phakathi kwazo ngokuvamile okuyi-giant cell temporal temporal or temporal arteritis (GTA). Elinye igama le-pathology isifo sikaHorton, ngokuhlonipha udokotela owamchaza kuqala.
Lesi sifo sitholwa ikakhulukazi asebekhulile, sithinta imishanguzo yobukhulu obuphakathi nendawo enkulu. Ezindongeni zabo, inqubo yokuvuvukala iqhubeka, eqhubeka kancane kancane. Ngokuhamba kwesikhathi, izitsha zincane ngokusungulwa kwe-thrombi futhi kunezifo ezihlukahlukene zokujikeleza kwe-circulatory.
Izimpawu zezifo zikaHorton
I-pathology echazwe iqala ngokujulile noma ihlukumeza, ivame ukuqala emva kokudluliswa kokutheleleka okunamandla kokuphefumula kwesandulela ngculazi. Izimpawu zokuqala ze-GTA:
- ikhanda;
- i-myalgia;
- umkhuhlane;
- ubunzima bokuhamba kwemisipha nolimi.
Izimpawu eziyinhloko ze-arteritis yesikhashana zihlanganisa izinhlobo ezintathu zemibonakaliso yemitholampilo:
Ukuxwala:
- ukushisa;
- i-anorexia;
- i-polymyalgia ye-rheumatic ;
- ikhanda;
- ukukhathala;
- ubuhlungu lapho ngifuna.
Ukuphazamiseka kwe-Vascular:
- Ama-neodules esikhumbeni se-scalp;
- ukuhlanganiswa kwe-artery parietal and temporal arteries;
- ubuhlungu lapho kutholakala khona izitsha ezimele.
3. Ukunqotshwa kwezitho ezibukwayo:
- kuncishiswe ubuciko obubonakalayo, kuze kube sekuphofukeni okungazelelwe;
- i-ischemic neuropathy ye-nertic optic.
Ukuwohloka kwemisebenzi yamehlo akukhona ngokushesha, kodwa emva kwamasonto amabili kuya kwengu-2 noma izinyanga ezimbalwa kusukela ekuqaleni kokuthuthukiswa kwezilwane, kanye nokukhululwa kwesifo sikaHorton. Izinguquko ezinjalo azitholakali, ngakho-ke kubalulekile kuzo zonke iziguli ezine-GTA ukuhlola njalo isimo se-fundus.
Ukuhlolwa kwegazi ngesifo sikaHorton
Isisekelo sokuxilongwa yisifo sokuhlolwa kwegazi eliphelele. Emiphumeleni yalokhu kuhlaziywa, izinqubo ezilandelayo ziphawulwe:
- i-hypoemromic anemia ;
- I-ESR ingaphezu kuka-50 mm / h;
- i-leukocytosis;
- umsebenzi owandayo we-enzyme e-hepatic;
- i-hypoalbuminemia;
- amazinga akhule we-IgG (ngezinye izikhathi).
Ukwelashwa kwezimpawu nezimbangela zesifo sikaHorton
Indlela kuphela ephumelelayo yokwelashwa kokuvuvukala kwezindonga zamathambo nge-GTA ukusebenzisa ama-hormone e-corticosteroid, ikakhulukazi i-Prednisolone. Ezimweni ezimbi, uhlelo lokwelapha lusekelwa omunye umuthi, i-Metiprednisolone.
Inkambo yokwelapha iqhubeka isikhathi eside, ngemuva kokukhululeka kwenqubo yokuvuvukala okucatshangwayo ukuthi kunconywa ukuthatha imithi yezinye izinyanga eziyisithupha kwisilinganiso sokulondoloza. Kuphela lapho kungekho khona izimpawu ze-Horton's syndrome ezinyangeni ezingu-6, ukwelashwa kuqedwe ngokuphelele.