I-myopathy iyisifo esingapheli se-neuromuscular esibangela ukulimala kwezicubu zomzimba. Isizathu sokwemyopathy yisiyaluyalu somzimba . Ucwaningo lwesayensi lwakamuva lubonisa ukuthi izibilini ezingenalutho zakhiwa emangqamuzaneni omzimba, futhi amafayili alahlekelwa amino acid adingekayo, ama-enzyme, i-creatine, abhujiswa futhi afe.
Izimpawu zokwehluleka
Ama-myopathies afaka kokubili izifo ze-neuromuscular heritage kanye ne-neuromuscular syndromes kwezinye izifo ezithile ze-somatic ne-neurological. Izimpawu ezijwayelekile zazo zonke izinhlobo zokwehluleka komzimba ziyizintuthwane ezibuthakathaka kanye nezinkinga zokuhamba.
Izimpawu ze-Duchenne myopathy
Isifo esivame kakhulu isifo se-Dodyscrophy sikaDuchesne. Kukhona isifo kuphela kubafana futhi sisakazwa ngesifo sofuzo esitholakala kumama. Kakade eminyakeni yokuqala yokuphila kukhona ukugaya emakhono amamoto, ubuthakathaka bemisipha yendawo ye-hip. Esikhathini esizayo kukhona ukubuthakathaka kwemisipha ye-trunk kanye nebhande lehlombe, kanye nemisipha yokuphefumula. Kungase kube khona i-lordosis (i-pathology yomgogodla), ukunciphisa imisipha yamathole. Ekuqaleni kokukhula, iningi leziguli liyeke ukuhamba ngokuzimela, zihlakulela izibonakaliso zokugulisa inhliziyo, ingqondo ayihambisani nemigomo yobudala, i-motility yamathumbu iphazamiseka. Iziguli azihlali isikhathi eside, zifa lapho zineminyaka engama-30 ngenxa yokungaqiniseki komzimba noma ukungenwa kwamaphalenda.
Izimpawu ze-steroid myopathy
Isizathu se-syoidal myopathy yinto ekhuphukayo ye-glucocorticosteroids egazini ngenxa yokukhiqizwa ngokweqile kwe-cortex yabo engakahle. I-hormone ingase futhi ikhule kwiziguli ezithola glucocorticosteroids isikhathi eside ekwelapheni izifo ezihlukahlukene. Izingqinamba ezisemtholampilo ezisemtholampilo zihambisana nokushintsha ekubukeni kwesiguli. Ngokusobala ukufakwa kwezicubu ze-adipose ebusweni, entanyeni, emzimbeni ophezulu (ngokuyinhloko phezu kwama-clavicles). Ingxenye engezansi yomzimba ayishintshi, okuholela ekukhusheni okucacile komzimba. Iziguli zizwa ubuthakathaka obubuthakathaka kanye nezinsizwa, ziphulukisa kancane amanxeba, kunezifo ezithathelwanayo. Isici sesici yi-striae - welula amanothi esikhumbeni, esivela ekukhuphukeni kwe-capillaries. Izingane zihlushwa ukulahlwa kokukhula, kubantu abadala kukhona ukuphazamiseka kwesigaba socansi. Ngeziguli zesifo sengqondo se-steroid ziyakwazi ukucindezeleka, ukuphazamiseka kwengqondo.
Izimpawu zokwehla kokudakwa ngokweqile
Ukuzizwa ngophuzo oludakayo kubonakala kubantu abavame ukusebenzisa kabi utshwala. Ngenxa yomphumela onobuthi we-ethyl emzimbeni, amangqamuzana omzimba we-muscle fibre of the skeleton nezitho zangaphakathi afa, futhi i-necrosis encane-iphuzu iqala. Izidakamizwa ezingapheli zikhononda ngalokhu:
- ukukhathala;
- ukuphoqwa kweminwe nezinzwane;
- ukuzwa kobunzima esifundeni somlomo wesibeletho.
Khona-ke zikhona izigumbane zobusuku, ukwephulwa kokubambisana. Kuyinto ukuzamazama okukhulu kwezandla. Imisipha kancane kancane iba yi-flabby, i-lethargic, ayikwazi ukuhlushwa. Indlela indlela yokudakwa ngokweqile ebonakala ngayo ifana nezimpawu zamanye ama-myopathies.
Kubalulekile ukuthi uma kuvela izimpawu ze-myopathy, xilonga ngokushesha