Phakathi kwezifo ezivame kakhulu ezibangelwa ukuguqulwa kwezakhi, i-cystic fibrosis yamaphaphu iphezulu ohlwini. Lezi zifo zihlobene nokuphulwa kwemfihlo eyimfihlo eyenziwa izitho zangaphakathi, okuholela ekunqothulweni kwesimiso sokuphefumula kanye nomgudu wamathumbu.
Isifo sofuzo se-cystic fibrosis
Lesi sifo esibuzwayo sibizwa nangokuthi i-cystic fibrosis. Kubonakala ngokuphakama okukhulu kanye nokuqina okunamandla kwe-mucus, okuhlanganisa izitho ezingenalutho. Njengenqubo yale nqubo, ukufihla kuyagcina, futhi amabhaktheriya e-pathogenic abangela ukuvuvukala kwande ngokuphindaphindiwe.
I-fibrosis yama-cystic yamaphaphu inesisusa esisodwa - umonakalo ku-chromosome yesikhombisa (ingalo ende). Ngokwezibalo, umphathi wesifo nguye wonke umuntu wamashumi amabili emhlabeni. Amathuba esi sifo angama-25%, uma nje abazali bobabili banegesi elimelekile.
Kunezinhlobo ezingu-3 zalesi sifo:
- i-cystic fibrosis yamathumbu;
- i-pulmonary noma i-cystic fibrosis yokuphefumula;
- uhlobo oluxutshwe (i-cystic fibrosis yamaphaphu).
I-cystic fibrosis yamaphaphu - izimpawu
Izimpawu eziyinhloko zesifo:
- ukuphuma kwe-viscous, sputum obukhulu ngesikhathi sokukhwehlela;
- ukuqhuma njalo kwe-pneumonia, i-bronchitis, i-pneumonia;
- ukuphazanyiswa kwamathumbu;
- ukuphelelwa amanzi;
- ubuhlungu, ubuhlungu esiswini;
- ukwandisa isifiso ngesisindo esanele nokuthuthukiswa ngokomzimba;
- izifo zobulili;
- i-pancreatitis ;
- ukuqina kweminwe ezandleni;
- isifo sesibindi;
- isifo sikashukela mellitus;
- i-sinusitis ;
- ukwehluleka kwamathambo;
- ukuphinda kwamathumbu (ngokuqondile).
Ifomu le-pulsary ye-cystic fibrosis ibonakala eminyakeni emibili yokuphila, ibonakala ngesibalo esikhulu semfihlo phakathi ne-bronchi encane yengane.
I-Cystic Fibrosis - Ukuxilongwa Nokuhlaziywa
Ukuxilongwa kwenziwa nge criteria ezine eziyinhloko.
Okokuqala, ukutholakala kofuzo olulimalayo kubazali kanye namacala okukhubazeka emndenini kuyahlolwa. Imiphumela emihle, kanye nokutholakala kwezinqubo ezivuvukala ezingapheli emaphashini nase-bronchi, ukuba khona kwamathumbu emathumbu, kunesizathu sokuqhuba ukujuluka kwesisu. Iqukethe ekunqumeni izinga lesawoti emthonjeni okhishwe yi-pores. Ukwenza inqubo, indawo encane engalweni (ngaphezulu kwesigqoko) iphathwa ngesidakamizwa esikhethekile esibizwa ngokuthi i-pilocarpine. I-electrode ifakwe kule ndawo, eyenza ukukhululwa kwesithukuthuku, okuhlukaniswe ngepulasitiki noma izicubu zokugcina ukushisa, okudala umphumela we-sauna. Ngemuva kwemizuzu engaba ngu-40, uketshezi olukhiqizwa lufakwa ekuhlaziyweni kasawoti. Uma izinga lalo lidlula umkhawulo osungulwe, kutholakala ukuxilongwa kokugcina.
I-cystic fibrosis yemithi yokwelashwa
Isifo sesifo asivumeli ukuba siphulukise ngokuphelele, ukwelashwa kuhloswe ekuqedeni izimpawu ezihlelekile futhi kudinga indlela ehlanganisiwe. Ukwelashwa kuqukethe imisebenzi elandelayo:
- izifundo ezimide zama-antibiotics;
- ukwamukela ama-mucolytics;
- i-kinesitherapy;
- Ukufakwe kwe-horticone ye-corticosteroid kanye ne-beta mimetics;
- ukusetshenziswa kwe-bronchodilator;
- ukwenza umzimba wokuphefumula;
- ukulungiswa kokudla nokunyuka kwesabelo samalanga onke ngo-10-15%;
- amanzi emiphakameni aphephile;
- bug-massage;
- ukwamukela amavithamini nama microelements.
Eyingozi kakhulu futhi ephumelela kakhulu okwamanje indlela yokwelashwa ukuguqulwa kwamaphaphu. Ngaphezu kwalokho, ucwaningo lwezokwelapha luqhutshwa njalo ukuze lungisole isakhi sofuzo esonakele kakhulu ngokusebenzisa ama-virus adalwe ngokuhlakanipha.