I-cystic fibrosis yamaphaphu

Phakathi kwezifo ezivame kakhulu ezibangelwa ukuguqulwa kwezakhi, i-cystic fibrosis yamaphaphu iphezulu ohlwini. Lezi zifo zihlobene nokuphulwa kwemfihlo eyimfihlo eyenziwa izitho zangaphakathi, okuholela ekunqothulweni kwesimiso sokuphefumula kanye nomgudu wamathumbu.

Isifo sofuzo se-cystic fibrosis

Lesi sifo esibuzwayo sibizwa nangokuthi i-cystic fibrosis. Kubonakala ngokuphakama okukhulu kanye nokuqina okunamandla kwe-mucus, okuhlanganisa izitho ezingenalutho. Njengenqubo yale nqubo, ukufihla kuyagcina, futhi amabhaktheriya e-pathogenic abangela ukuvuvukala kwande ngokuphindaphindiwe.

I-fibrosis yama-cystic yamaphaphu inesisusa esisodwa - umonakalo ku-chromosome yesikhombisa (ingalo ende). Ngokwezibalo, umphathi wesifo nguye wonke umuntu wamashumi amabili emhlabeni. Amathuba esi sifo angama-25%, uma nje abazali bobabili banegesi elimelekile.

Kunezinhlobo ezingu-3 zalesi sifo:

I-cystic fibrosis yamaphaphu - izimpawu

Izimpawu eziyinhloko zesifo:

Ifomu le-pulsary ye-cystic fibrosis ibonakala eminyakeni emibili yokuphila, ibonakala ngesibalo esikhulu semfihlo phakathi ne-bronchi encane yengane.

I-Cystic Fibrosis - Ukuxilongwa Nokuhlaziywa

Ukuxilongwa kwenziwa nge criteria ezine eziyinhloko.

Okokuqala, ukutholakala kofuzo olulimalayo kubazali kanye namacala okukhubazeka emndenini kuyahlolwa. Imiphumela emihle, kanye nokutholakala kwezinqubo ezivuvukala ezingapheli emaphashini nase-bronchi, ukuba khona kwamathumbu emathumbu, kunesizathu sokuqhuba ukujuluka kwesisu. Iqukethe ekunqumeni izinga lesawoti emthonjeni okhishwe yi-pores. Ukwenza inqubo, indawo encane engalweni (ngaphezulu kwesigqoko) iphathwa ngesidakamizwa esikhethekile esibizwa ngokuthi i-pilocarpine. I-electrode ifakwe kule ndawo, eyenza ukukhululwa kwesithukuthuku, okuhlukaniswe ngepulasitiki noma izicubu zokugcina ukushisa, okudala umphumela we-sauna. Ngemuva kwemizuzu engaba ngu-40, uketshezi olukhiqizwa lufakwa ekuhlaziyweni kasawoti. Uma izinga lalo lidlula umkhawulo osungulwe, kutholakala ukuxilongwa kokugcina.

I-cystic fibrosis yemithi yokwelashwa

Isifo sesifo asivumeli ukuba siphulukise ngokuphelele, ukwelashwa kuhloswe ekuqedeni izimpawu ezihlelekile futhi kudinga indlela ehlanganisiwe. Ukwelashwa kuqukethe imisebenzi elandelayo:

Eyingozi kakhulu futhi ephumelela kakhulu okwamanje indlela yokwelashwa ukuguqulwa kwamaphaphu. Ngaphezu kwalokho, ucwaningo lwezokwelapha luqhutshwa njalo ukuze lungisole isakhi sofuzo esonakele kakhulu ngokusebenzisa ama-virus adalwe ngokuhlakanipha.