I-Badda-Chiari Syndrome

Lesi yisifo esingavamile. I-Badda-Chiari syndrome itholakala kumuntu oyedwa ngamakhulu ayikhulu. Lesi sifo sihlobene nokusebenza kabi kwesibindi. Ngokuvame ukutholakala kunabesifazane abaphakathi. Kodwa ngezikhathi ezithile ngesifo, iziguli ezincane nazo ziyahlangana.

Izimbangela zeBadda-Chiari Izifo

I-Badda-Chiari syndrome - ukuvinjelwa kwemithanjeni ye-hepatic. Ngalesi sifo, i-veins iminyene, ngenxa yokuthi igazi elivamile eligeleza esibindi liphazamiseka. Ngesikhathi esifanayo, umzimba awukwazi ukusebenza kahle.

Isizathu saleso sifo singase sibe ezinye ze-anomalies ezingenasifo esibelethweni se-veptic hepatic. Izinto ezilandelayo zifaka isandla ekuthuthukiseni i-syndrome:

I-Budda-Chiari syndrome ingathuthuka ngemuva kokusebenzisa isikhathi eside isikhathi sokubeletha kokubeletha noma ngemuva kokungenelela kokuhlinzwa. Ngezinye izikhathi lesi sifo sibonakala ngemuva kokukhulelwa nokubeletha.

Izimpawu ze-Badd-Chiari Syndrome

Ukuhlukanisa phakathi kwamafomu ajwayelekile nesifo esingapheli sesifo. Lokhu kuvele kwenzeka ezimweni eziningi. Ukubonakaliswa kwesifo kungahlukahluka kuye ngokuma kwayo. Ngakho-ke, isibonelo, ukugula okungapheli kukaBudda-Chiari kungase kuhlale kungabonakali. Futhi ngezigaba kamuva kunezibonakaliso ezinjalo njengezinambuzane, ukuhlanza, izinzwa ezibuhlungu ku-hypochondrium efanele. Isibindi kwanda futhi kuqina. Ngezinye izikhathi i-cirrhosis iqala.

Ifomu elimangalisayo likaBudd Chiari liboniswa izimpawu ezifana nobuhlungu obukhulu nokuhlanza. Uma lesi sifo sisakazeka emithanjeni engezansi engezansi, isiguli singase sibe imilenze yokuvuvukala, i-reticulum ye-vascular ibonakala ngodonga lwangaphakathi lwesisu. Lesi sifo siphuthuma kakhulu, futhi kungakapheli izinsuku ezimbalwa isiguli singatholakala nge-ascites.

Izimpawu zezifo eziningi zesibindi, isibonakaliso - i-jaundice - ayidlangalaleni ku-Buddha-Chiari syndrome.

Ukwelashwa kwe-Badda-Chiari syndrome

Esikhathini sokuqala, ukwelashwa kwezokwelapha kuhlongozwa, okubandakanya ukusetshenziswa kwezidakamizwa kanye nama-coagulants, kodwa akusho njalo ukunikeza imiphumela emihle.

Ngokuvamile, i-Badda-Chiari syndrome iphathwa ngokuhlinzwa endaweni yesibhedlela. Okukhethwa kukho konke ukusebenzisa uhlelo lwe-anastomosis. Ezimweni ezinzima kakhulu, ukufakelwa kwesibindi kungadingeka.