I-atrophy yama-spinal muscular iyisifo sofuzo esithinta ingxenye yesistimu yezinzwa ezibhekene nokulawula izithintelo zemisipha engapheli. Lokhu kungenxa yokufa kwamangqamuzana omzimba we-spinal cord - ama-motoneurons. Lesi sifo siqala eminyakeni ehlukene, futhi umuntu ngamunye unomuntu ngamunye.
Izimpawu zomzimba we-spinal muscular atrophy
Kunezibonakaliso eziyinhloko zesifo. Ngeshwa, zivela kuphela uma lesi sifo sesiqalile ukuqhubeka. Lokhu kufaka:
- ubuthakathaka emaphethelweni , ikakhulukazi phansi;
- imisipha ye-muscle, ukuthuthumela kancane kweminwe ngezandla;
- shintsha ngesakhiwo sezingcuba;
- izinkinga ngesifunda se-pelvic.
I-atrophy yama-spinal muscular ibhekene nezinkinga nemisipha yemilenze, intamo nenhloko. Iziguli zingase zibe nesifo ngokunyakaza okungaqondakali: ukuhamba, ukugwinya, ukunyakaza kwenhloko. Ngesikhathi esifanayo, uzwela luhlala futhi alukho izinkinga ekuthuthukiseni kwengqondo.
Ukuxilongwa komzimba we-spinal muscular atrophy
Ukuze uhlole okokuqala, udinga ukuya ku-neurologist noma i-traumatologist. Lesi sifo ngokwawo sithuthuka ngokushesha. Ngakho-ke, ukuxilongwa kokuqala kufanele kugcwaliswe ngokushesha ngangokunokwenzeka. Ngenxa yokuthi lesi sifo sidluliselwa ngefa, umlando wesihlobo esilandelayo uqale wafundiswa.
Njengesijwayelekile, ukuhlolwa okujwayelekile kunikezwa. Ngokuvamile kudingeka udinga olunye ulwazi oluthile , yenza i-ray ray yamathambo kanye nezicubu zomzimba. Ochwepheshe bathola ijubane lesi sifo esikhula ngayo. Ngaphezu kwalokho, ikhono lokusebenza kanye nemisebenzi eyenziwa imisipha ingacacisiwe.
Izimbangela ze-muscle atrophy yomgogodla
Muva nje, lesi sifo saqala ukuzibonakalisa kaningi. Yingakho ochwepheshe abaningi bezama ukuthola izimbangela zangempela zenzeke. Into yukuthi kunomunye wabantu abangamashumi amahlanu igugu eliguquliwe
Ukwelashwa kwe-spinal muscular atrophy
Ukwelashwa kwalesi sifo kuhloswe ekususweni kwezimpawu. Kubalulekile ukushintsha ukudla nokuphila. Ebizwa ngemithi yokukhanya, izinqubo eziqhubekayo zomzimba kanye nokusikhipha umzimba.