Isifo sikaBehcet

Isifo sikaBehcet yisifo esibuhlungu esingapheli, isifo esivame kakhulu eJapane naseMedithera. Ngokuvamile kuvame kubantu abaneminyaka engama-30 kuya kwengu-40. Lesi sifo singokwesigaba se-vasculitis futhi sinesifo se-etiology esingaziwa.

Izimbangela zezifo zikaBehcet

Ukuthuthukiswa kwalesi sifo kuhlotshaniswa nezici eziningana zokubeka phambili, phakathi kwazo okulandelayo:

Iningi lezazi zikholelwa ukuthi ukuqala kwesifo sikaBehçet kubangelwa yizici ezithathelwanayo, futhi esikhathini esizayo, izindlela ezizenzekelayo zihlanganiswe kubo, uma kunikezwe indawo yokuzalwa.

Izimpawu zesifo sikaBehcet kubesifazane

Lesi sifo sibonakala nge-polysimptomicity. Kulesi simo, izibonakaliso ezinkulu, lapho ungenza khona ukuxilongwa okunembile, zihlotshaniswa nomonakalo emagqumeni omzimba omlomo kanye nezitho zangasese, kanye nezinqubo zokuvuvukala emehlweni. Cabanga konke ukubonakaliswa kwesifo sikaBehçet ngokuningiliziwe.

Ukulimala komlomo womlomo

Ekuqaleni, ama-vesicle amancane anezinto ezifiphalayo avela ezindebeni, esibhakabhakeni, emlimini, ezinsini, e-pharynx, emaphethelweni angaphakathi, abuye avuleke. Esikhundleni sama-vesicles, ama-round, izilonda ezibuhlungu (aphthae) zombala ogqamile obomvu zakhiwa, ubukhulu bawo obufinyelela ku-2 cm ububanzi. Ukuphulukiswa kwezilonda kwenzeka cishe ngenyanga, futhi izikhathi ezingu-3-4 ngonyaka izilonda zesisu.

Izilonda zesisu

Abesifazane embranini yomsindo wezilonda nezifo ezinamazinyo, ngokuvamile ezibuhlungu, afana nalabo abonakala emlonyeni. Ngemuva kokuphulukiswa, izibazi zingase zihlale endaweni yazo.

Ukuphazamiseka kombono

Lezi zibonakaliso zivela amasonto ambalwa emva kwezimpawu ezisendlini yomlomo. Iziguli zingathuthuka ukuvuvukala komzimba we-iris ne-ciliary we-eyeball, ukuvuvukala kwezingqamuzana ze-vascular and mucous iso, ukuvuvukala kwe-cornea. Ngokuvamile kunezibonakaliso ezilandelayo: photophobia, umbono obonakalayo, ukukhala okukhulu.

Ukubonakaliswa okukodwa

I-eyerythema engavamile, i-pyoderma, i-papulo-i-vesicular rash ingase ivele. Kanti kwezinye izimo, kutholakala ukulahleka kwezinwele, i-subungual panaritium.

Izinkinga zesistimu ye-musculoskeletal

Kukhona ukuthuthukiswa kwe-arthritis (izikhathi eziningi eziphansi) ngaphandle kwezinto ezilimazayo.

Izimpawu ze-neurological

Kukhona izimo ezilimazayo zokulimala kwamantombazane, ukuthuthukiswa kwe-meningoencephalitis, i-edema ye-optic nerve disk, ukubukeka kwe-hemiparesis.

Izinguquko zokuvuvukala eziyinkimbinkimbi

Imfanelo yokuthuthukiswa kwe-vasculitis, i-thrombophlebitis yemilenze emilenzeni, isifo se-hepatic ne-thromboembolism yomshini we-pulmonary, aneurysm aortic, njll.

Njengoba izilonda zesisu, izinhliziyo namaphaphu, kungenzeka kube nezimpawu ezinjalo:

Ukwelashwa kwezifo zikaBehcet

Ukwelashwa kwesifo sikaBehcet, okokuqala, kuhloswe ukukhulisa impilo yesiguli, ukufeza ukuxolelwa isikhathi eside nokuvimbela izinguquko ezingenakuguquka ezingxenyeni zangaphakathi.

Ukubonakaliswa okulindile kwe-Behcet's syndrome emgodini womlomo nangokwezitho zangasese kuncike kokwelashwa kwendawo ngokusetshenziswa kwe- glucocorticosteroids , izixazululo ze-antiseptic, futhi ngezinye izikhathi - ama-antipodal agents. Kanti futhi ekwelapheni lesi sifo, ama-cytostatic agents, immunosuppressors, amavithamini angabekwa. Umonakalo we-Vascular uphathwa ngezindlela zokuhlinzwa. Iziguli eziningi zinqunywe i-extracorporal hemocorrection. Ukwelashwa kwenziwa ngaphansi kokuqondiswa kwezokwelapha njalo.