Ukudla okungalungile, ukuphila esimweni sokucindezeleka, ukuwohloka kwemvelo - konke lokhu kuthinta impilo yomuntu ongcono. Ngenxa yalokho, lesi sifo esibangelwa ukwehluleka kwesistimu ethile emzimbeni saba njalo. Lokhu kufaka phakathi i-autoimmune (idiopathic) thrombocytopenia noma isifo sikaVerlhof.
Izinhlobo nezimbangela ze-thrombocytopenia ye-autoimmune
Lesi yisifo segazi, lapho inani lamaplatelet liyancipha ngoba iqiniso lokuthi ukuzivikela komzimba kuqala ukukhiqiza ama-antibodies ngaleli qembu lamaseli. I-thrombocytopenia ye-autoimmune ivela:
- okuyisisekelo, okungukuthi, ephuma ngokwayo;
- eyesibili, kubonakale ngenxa yokunqotshwa kwesimiso somzimba sokuzivikela ngenxa yezifo ezifana nomdlavuza we-lymph nodes, i-HIV, i-rubella, i-autoimmune hepatitis, njll;
- izidakamizwa, okwenzeka ngemuva kokuthatha imithi noma izidakamizwa zezinambuzane.
Izimpawu ze-thrombocytopenia ye-autoimmune
Uphawu oluphawulekayo lokuthuthukiswa kwalesi sifo lubukeka bezinhlobo eziningi zezinsiza ezinjengamaphuzu amancane. Ngokuvame ukutholakala esikhunjeni se-trunk kanye nemiphetho. Futhi ukuqhuma kwesimiso kungaqala. Ngaphezu kwalokho, kukhona ukuphuma kwe-mucosa emithonjeni yomlomo neyomlomo.
Njengoba ama-platelet anesibopho sokuqeda igazi, kusho ukuthi uma kutholakala lokho, uma isikhumba sinakele, ukuphuma kwegazi akukwazi ukumiswa isikhathi eside. Lokhu kuphazamisa nokuthi isikhathi sokuya esikhathini sesifazane siningi kakhulu, kanti emanzini kukhona igazi.
Uma kungekho izinkinga ezingenakuqhathaniswa ezazibonwa (isibonelo, isifo socerebral hemorrhage), ukuchazwa kweziguli ezine-autoimmune thrombocytopenia kunethemba. Lesi sifo sizodlula ngokwayo, noma ukubuyiswa kuyofika ngenxa yomuthi.
Ukwelashwa kwe-thrombocytopenia ye-autoimmune
Ukwelashwa okuyinhloko kwe-autoimmune thrombocytopenia kuhloswe ekunciphiseni ukukhiqizwa kwama-autoantibodies okubhubhisa amaplatelets, kodwa endaweni yokuqala kufanele kutholakale. Kulokhu, ukuhlolwa okuningi kufanele kuhanjiswe:
- ukuhlolwa kwegazi jikelele ;
- ukuhlaziywa okujwayelekile komchamo;
- ukuhlolwa ngokwendlela kaSteffen (ukuzimisela kwenani lama-antiglobulins);
- Ukuhlolwa kwe-Dickson (ukubalwa komuntu wokulwa nomuntu).
Ngezinga eliphansi le-thrombocytopenia ye-autoimmune, izidakamizwa ze-hormonal ezivela eqenjini le-glucocorticosteroids (ngokuvamile i- prednisolone ngesilinganiso se-1 mg ngekgrimu yesisindo somzimba) inqunywe. Thatha idinga ukutakula ngokugcwele, bese unciphisa kancane kancane umthamo. Uma ukwelashwa okunjalo akusizi, odokotela benza umsebenzi wokukhipha isilwane.