Galactosemia ezisanda kuzalwa

Ngeshwa, ngokuvamile i-galactosemia ezinganeni ezisanda kuzalwa aziqapheli. Kodwa-ke, isimo seziguli ezinezifo ezithathelwana ngokobuciko sehla kakhulu ngokushesha ezinsukwini zokuqala zokuphila kwazo. Ngosuku lwesine lwenqubo engalawuleki yesifo, abantwana abanjalo abakwazi ukuphuza. Ukuziphatha kwabo kokunganaki, okubonakala kude, kungenxa yesimo esibi sangaphakathi - banesibindi sokwanda kwesibindi, i-jaundice ivela, uketshezi luhlanganisa izicubu.

I-Galactosemia yisifo esibi kakhulu, asikwazi ukwelashwa ngendlela izifo ezibangelwa amagciwane eziphathekayo eziphatheka ngayo, kodwa kungenzeka ukuthi udale ingane enezifo ezibizwa ngokuthi yizimo eziphilayo ezifanayo njengalezi zontanga zakhe ezinempilo. Kulesi simo, usizo olulodwa olunganikezwa ingane ukuthi ufunde indlela yokulandela ukudla okukhethekile okudingekayo kumntwana.

Izimbangela Nezimpawu ZeGalactosemia

I-Galactosemia iyisifo esithatha isizalo (esibhedlela) esibangelwa ukungasebenzi komzimba kanye nokuholela ekutholeni i-galactose emzimbeni. Njengomphumela wesifo sofuzo ku-galactosemia, ukuguquguquka kwe-galactose kuya kwe-glucose kuhlulekile.

Iningi lezingane ezisanda kuzalwa ezine-galactosemia zinesisindo esikhulu somzimba - okungaphezu kuka-5 kilogram. Ngemva kokudla, bahlanza kakhulu, futhi ngezinye izikhathi uhudo. Isimo seziguli sihlabeka ngokushesha ngenxa yokwanda kwesibindi, i-spleen, i-ascites (isimo lapho umkhuhlane uqoqa khona emgodini wesisu). Kamuva, izimpawu zingase zihambisane ne-clouding ye-lens (noma i-cataract). Ngaphandle kokwelashwa, izinsana ezine-galactosemia zingase zife ngenxa ye-bacterial sepsis, evame ukuqala nalesi sifo. Kodwa-ke, ezimweni zanamuhla, iziguli ezinezibonakaliso zokuqala ze-galacosemia ziyasizwa ngokushesha ngabasebenzi bezokwelapha.

Ukwelashwa kwe-galactosemia - ukudla okuqinile

Isisekelo sokwelashwa kwezingane ezigulayo ukudla okungenamsoco. Khumbula ukuthi nakuba izingane ezingavunyelwe i-lactose zivunyelwe ukusebenzisa ubisi lwe-lactose, imikhiqizo emisha ye-lactose engenamvume ayivunyelwe izinsana ezine-galactosemia. Ekudleni kwengane, kubalulekile ukugwema ubuncane obukhona ubisi kanye neziqhamo zalo, kubandakanya ukuxuba ubisi - abakwazi ukufaka umzimba womntwana wabo ngaphakathi. Izingxube ezingasetshenziselwa i-galactosemia yizingxube ze-soy nobisi lwe-almond.

Noma kunjalo, khumbula ukuthi ukwenqatshwa kwemikhiqizo yobisi njengokweshizi, i-yogurt, ukhilimu, ibhotela, kanye nemikhiqizo equkethe ngisho namathrekhi ebisi - lokhu akuyona isilinganiso sesikhashana. Kule mikhiqizo, isiguli esinomdlavuza wegalactosemia kuzodingeka sigweme konke ukuphila kwakhe, sigweme ukufaka imikhiqizo enjengegargarine, isinkwa, amasoso kanye nemikhiqizo eqedile, lapho ubisi obungatholakala khona. Ungadangali, ungasebenzisa uhla olubanzi kakhulu lweminye imikhiqizo: inyama, inhlanzi, imifino, izithelo, amafutha omifino, amaqanda, okusanhlamvu okuhlukahlukene.