Izingane-Izintuthwane ... Ngesikhathi sokuqala ukuzwa le nkulumo, abaningi bavele bacabange ngamabhomu anemibala, behlupha phakathi kwezimbali nenjabulo yobuntwana, behluleka ukudumazeka okudabukisayo nokukhathazeka. Phakathi naleso sikhathi, ukuphila kwezingane ezine-butterfly syndrome akufani nhlobo inganekwane noma isithombe esihle. Kulesi sihloko sizokhuluma nge-congenital bullous epidermolysis - isifo esingavamile sofuzo esithinta isikhumba somzimba womuntu.
I-Epidermolysis ye-Bullous: Izimbangela
Ngokusemthethweni, abazali bezingane ze-butterfly bafunda ngokugula kwengane yengane yabo ezinsukwini zokuqala (ngisho namahora) emva kokuzalwa kwengane. Isikhathi sokuqala lesi sifo sachazwa ngasekupheleni kwekhulu le-19, ngo-1886.
Isizathu saleso sifo yisici esingokwemvelo esinqunyiwe isendlalelo se-epidermal sokukwazi ukwenza umsebenzi wokuzivikela. Lesi siphambeko sisatshalaliswa kubazali abathwali bayo abafihlekile, noma kuvela ngokuzenzekelayo. Ngenxa yalokho, zonke izikhumba (kufaka phakathi izibungu zamangcwaba) ziba buthakathaka kakhulu - ukuthinta kancane kungabangela umonakalo. Uma kungenjalo, izingane ezinjalo zijwayelekile - azihlezi ngemuva kokuthuthukiswa ngokomzwelo nangokwengqondo, zikhula ngendlela evamile futhi zingaba yingxenye egcwele yomphakathi.
Amaphethini wefa lelesi sifo ayengakabonakali - iziguli ezine-epidermolysis enezinyosi zingaba nezingane ezinempilo nezigulayo. ukucaca kwalesi sifo nokuthi ngaphambi kokuzalwa kwengane akunakwenzeka ukuyihlolisisa nganoma iyiphi indlela yokwelapha eyaziwayo - noma i- ultrasound ye-fetus noma izivivinyo ze-laboratory ziveza imiphumela.
Isikhathi esibucayi sokuphila kwezingane ezincane ze-butterfly sekuyiminyaka emithathu. Esikhathini esizayo, ngokuphathwa kahle nokunakekelwa, isikhumba siba kancane kancane, siyaqina, nakuba singafinyeleli amandla esikhumba somuntu ovamile. Ngaphezu kwalokho, izingane ezincane azikwazi ukuqaphela ubudlelwane obangela imbangela, azikwazi ukuchaza ukuthi akunakwenzeka, isibonelo, ukugwaza ngamadolo abo, ngoba isikhumba semilenze ngemva kwalokho "siphume" ngokuphelele, noma ugobe amehlo noma izihlathi.
I-epidermolysis ye-bullous: ukwelashwa
Inselele yezingane ze-butterfly kunzima, ngoba ukugula okubangela ukuba bahlupheke kakhulu kungenakuphulukiswa namuhla. Konke okungenziwa kubantwana abanjalo ukuzama ukuvikela isikhumba sabo esibucayi ekulimaleni (okuyinto enzima kakhulu), kanti uma kwenzeka kwenzeka kahle futhi ngesikhathi sokubheka. Kodwa naphezu kwalokhu, emazweni amaningi asethuthukile amasu okunakekelwa kweziguli kanye nezifundo zokwelapha okuhlala njalo, asebenza bakwazi ukuhola impilo evamile, ukuthola imfundo, ukuhola impilo yokuphila komphakathi ngisho nokudlala imidlalo.
E-CIS, lapho kutholakala ukuthi i-epidermolysis ye-bullous, ukuhlushwa kwegazi kuningi kakhulu, ngoba lesi sifo singavamile ngokweqile, odokotela abanaso isipiliyoni sokwelapha lezi ziguli, futhi kwezinye izimo ngisho nokusola ukuthi kukhona lesi sifo. Ngokuvamile abazali ngokwabo bayacindezela lesi simo, benze imithi yokwelashwa futhi bazama ukuphatha umonakalo esikhunjeni sezingane baby phytotherapeutic, amafutha okugcoba kanye nabakhulumi, bluehead nezinye izindlela zalolu hlobo. Akungadingeki ukuthi, emva "kokwelapha" okunjalo, izindleko zokubuyisela i-epidermis yokunyuka kwengane ibe yizilinganiso ze-cosmic, kanti ukunakekelwa okwanele okufika ngesikhathi kunzima nakakhulu, kodwa kubiza kakhulu. Izingane ze-Butterfly zidinga
Ngenxa yokuqwashisa kwezokwelapha nezenhlalakahle, ukungabi nolwazi lokunakekelwa nokwelapha, izingane eziningi ezine-epidermolysis enezinkunzi ziyafa zisencane.
Yiqiniso, ukunakekelwa kwesikhumba kanye nokuphila kwezingane ze-butterfly kuyahluka kakhulu kuye ngokuthi ubuhlungu besifo - buyinkimbinkimbi kangakanani futhi kukhulume kakhulu izimpawu, ukunakekelwa nokuphathwa kwengane kufanele kube ngokucophelela futhi kunembile.